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原发性免疫缺陷病(PID)—专业代理Bioporto产品

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品牌: BioPorto
起订: 10 盒
供货总量: 1000000 盒
发货期限: 自买家付款之日起 3 天内发货
所在地: 上海
有效期至: 长期有效
最后更新: 2022-02-15 14:02
浏览次数: 917
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公司基本资料信息
 
 
产品详细说明
上海惠诚生物物专业代理并分销BioPorto品牌与原发性 免疫缺陷病(PID)补体系统研究相关的单克隆抗体、抗原及ELISA试剂盒。免疫缺陷病是由免疫系统先天性发育障碍或后天损伤而致的一组综合征。由遗传 因素或先天性免疫系统发育不良造成的免疫功能障碍,称为原发性免疫缺陷病(PID)。由后天因素(如感染、营养、疾病、药物等)引起的免疫功能障碍,称为 继发性免疫缺陷病(SID)或获得性(acquired)免疫缺陷病。
补体系统是先天性免疫系统的一个组成部分,补体系统由多种不同的血浆蛋白组成,广泛参与机体微生物防御反应以及免疫调节,也可介导免疫病理的损伤性反应,是体内具有重要生物学作用的效应系统和效应放大系统。
甘露糖结合凝集素(MBL)
甘露糖结合凝集素(mannose binding lectin, MBL)是参加天然免疫的宿主防御分子,它能够通过凝集素途径激活补体系统和吞噬作用从而在宿主免疫防御中发挥重要作用。MBL基因多态性与多种疾病易感 性,严重程度以及预后密切相关,在免疫系统尚未成熟的儿童或同时存在原发或继发免疫缺陷患者,低表达MBL基因型与感染性疾病,自身免疫病的相关性尤其显 著。上海惠诚生物提供的MBL Oligomer ELISA试剂盒,用于人源血清或血浆中的功能性MBL水平;提供检测人、鸡、马、大鼠来源的MBL抗体,血清中的人源MBL抗原。
MBL ELISA 检测试剂盒
货号 产品名称 描述 包装规格 检测种属 检测样品 检测范围
KIT 029 MBL Oligomer ELISA Kit An ELISA for the determination of oligomerized MBL in human serum or heparin plasma 96 well Human Urine; plasma; serum; tissue extracts or culture media 0.50-40 ng/mL
MBL 单克隆抗体
货号 产品名称 规格 宿主 应用
HYB 131-01-02 Mannan-binding lectin (human, MBL) 200µl Mouse ELISA, WB, IHC-P, IHC-F
HYB 131-01-1 Mannan-binding lectin (human, MBL) 1ml Mouse ELISA, WB, IHC-P, IHC-F
HYB 131-01B-005 Mannan-binding lectin (human, MBL) 50µl Mouse ELISA, WB
HYB 131-10-02 Mannan-binding lectin (human, MBL) 200µl Mouse ELISA, WB
HYB 131-10-1 Mannan-binding lectin (human, MBL) 1ml Mouse ELISA, WB
HYB 131-11-02 Mannan-binding lectin (human, MBL) 200µl Mouse ELISA, WB, IP
HYB 131-11-1 Mannan-binding lectin (human, MBL) 1ml Mouse ELISA, WB, IP
HYB 131-14-02 Mannan-binding lectin (human, horse, pig, MBL) 200µl Mouse ELISA, WB
HYB 131-14-1 Mannan-binding lectin (human, horse, pig, MBL) 1ml Mouse ELISA, WB
HYB 131-18-02 Mannan-binding lectin (rat, MBL) 200µl Mouse ELISA, WB
HYB 131-18-1 Mannan-binding lectin (rat, MBL) 1ml Mouse ELISA, WB
HYB 182-01-02 Mannan-binding lectin (chicken, MBL) 200µl Mouse ELISA, WB, IHC
HYB 182-01-1 Mannan-binding lectin (chicken, MBL) 1ml Mouse ELISA, WB, IHC
MBL 抗原(血清)
货号 产品名称 包装规格 形式 存储条件 保质期
SER 101 MBL standard serum (human) - 1000 (AU) 1mL Freeze-dried, undiluted pooled human serum -20°C 2 years
SER 103 MBL oligomer deficient serum, B/C genotype (human) 1mL Frozen, undiluted human serum -20°C 2 years
其他补体激活途径相关因子
除MBL以外,西宝生物专业提供其他补体激活途径相关 因子的单克隆抗体:Complement C1-INH、C1s、C2、C3、C3d、C3a/C3a(desArg)、C9、C5、C5a/C5a(desArg)、C5b-9、C4;L- ficolin、H-ficolin、M-Ficolin;Factor D、Factor H、Factor B,Properdin,Glycoprotein-340等抗体。
货号 产品名称 规格 宿主 应用

ABS 002-09-02

Complement component C1s (human, pro- and activated enzyme)

200µl

Mouse

ELISA

ABS 002-09-1 Complement component C1s (human, pro- and activated enzyme) 1ml Mouse ELISA
ABS 002-49-02 Complement component C1s (human, pro- and activated enzyme) 200µl Mouse ELISA
ABS 002-49-1 Complement component C1s (human, pro- and activated enzyme) 1ml Mouse ELISA
ABS 004-22-02 Complement component C9 (human) 200µl Mouse ELISA, WB
ABS 004-22-1 Complement component C9 (human) 1ml Mouse ELISA, WB
ABS 004-53-02 Complement component C9 (human) 200µl Mouse ELISA
ABS 004-53-1 Complement component C9 (human) 1ml Mouse ELISA
CAM 008-01-02 Complement Component C3 (human) 200µl Mouse ELISA, IP, IAP
CAM 008-01-1 Complement Component C3 (human) 1ml Mouse ELISA, IP, IAP
CAM 072-18-02 Complement C4c 200µl Mouse ELISA, WB, IP
CAM 072-18-1 Complement C4c 1ml Mouse ELISA, WB, IP
DIA 011-01-02 Complement component C5b-9 200µl Mouse ELISA, WB (not applicable), IHC-F, IHC-P
DIA 011-01-1 Complement component C5b-9 1ml Mouse ELISA, WB (not applicable), IHC-F, IHC-P
DIA 011-01B-01 Complement component C5b-9 100µl Mouse ELISA
GAU 008-01-02 Complement factor D (human) 200µl Mouse ELISA, WB
GAU 008-01-1 Complement factor D (human) 1ml Mouse ELISA, WB
GAU 008-01B-01 Complement factor D (human) 100µl Mouse ELISA
GAU 010-04-02 Complement factor D (human) 200µl Mouse ELISA, WB
GAU 010-04-1 Complement factor D (human) 1ml Mouse ELISA, WB
GAU 013-16-02 Complement component C3a/C3a(desArg)/C3 (human) 200µl Mouse ELISA, WB
GAU 013-16-1 Complement component C3a/C3a(desArg)/C3 (human) 1ml Mouse ELISA, WB
GAU 017-01-02 Complement component C3a/C3a(desArg)/C3 (human) 200µl Mouse ELISA, WB
GAU 017-01-1 Complement component C3a/C3a(desArg)/C3 (human) 1ml Mouse ELISA, WB
GAU 017-01B-01 Complement component C3a/C3a(desArg)/C3 (human) 100µl Mouse ELISA
GAU 018-03-02 Complement factor H (human, ß1H-globulin) 200µl Mouse ELISA, WB, IHC
GAU 018-03-1 Complement factor H (human, ß1H-globulin) 1ml Mouse ELISA, WB, IHC
GAU 020-03-02 Complement factor H (human, ß1H-globulin) 200µl Mouse ELISA, WB
GAU 020-03-1 Complement factor H (human, ß1H-globulin) 1ml Mouse ELISA, WB
GAU 020-03B-01 Complement factor H (human, ß1H-globulin) 100µl Mouse ELISA
GAU 025-05-02 Anti-Complement component C5a/C5a(desArg) anaphylatoxin (human) 200µl Mouse ELISA, WB
GAU 025-05-1 Anti-Complement component C5a/C5a(desArg) anaphylatoxin (human) 1ml Mouse ELISA, WB
HAV 003-05-02 Complement component C3 (human) 200µl Mouse ELISA, WB
HAV 003-05-1 Complement component C3 (human) 1ml Mouse ELISA, WB
HAV 004-01-02 Complement component C3 (human), beta-chain genetic variant 200µl Mouse ELISA, WB
HAV 004-01-1 Complement component C3 (human), beta-chain genetic variant 1ml Mouse ELISA, WB
HYB 005-01-02 Complement component C3 (human) 200µl Mouse ELISA, WB
HYB 005-01-1 Complement component C3 (human) 1ml Mouse ELISA, WB
HYB 008-02-02 Complement factor B (human) 200µl Mouse ELISA, WB
HYB 008-02-1 Complement factor B (human) 1ml Mouse ELISA, WB
HYB 008-06-02 Complement factor B (human) 200µl Mouse ELISA, WB
HYB 008-06-1 Complement factor B (human) 1ml Mouse ELISA, WB
HYB 008-06B-01 Complement factor B (human) 100µl Mouse ELISA
HYB 029-02-02 Complement component C5 (human) 200µl Mouse ELISA, WB
HYB 029-02-1 Complement component C5 (human) 1ml Mouse ELISA, WB
HYB 029-03-02 Complement component C5 (human) 200µl Mouse ELISA, WB
HYB 029-03-1 Complement component C5 (human) 1ml Mouse ELISA, WB
HYB 030-08-02 Complement component C3d (human) 200µl Mouse ELISA, WB
HYB 030-08-1 Complement component C3d (human) 1ml Mouse ELISA, WB
HYB 050-04-02 Complement component C2 (human) 200µl Mouse ELISA, WB
HYB 050-04-1 Complement component C2 (human) 1ml Mouse ELISA, WB
HYB 050-05-02 Complement component C2 (human) 200µl Mouse ELISA, WB
HYB 050-05-1 Complement component C2 (human) 1ml Mouse ELISA, WB
HYB 050-08-02 Complement component C2 (human) 200µl Mouse ELISA, WB
HYB 050-08-1 Complement component C2 (human) 1ml Mouse ELISA, WB
HYB 061-01-02 Complement factor I (human) 200µl Mouse ELISA, WB
HYB 061-01-1 Complement factor I (human) 1ml Mouse ELISA, WB
HYB 118-02-02 Complement component C3 (rat) 200µl Mouse ELISA, IHC
HYB 118-02-1 Complement component C3 (rat) 1ml Mouse ELISA, IHC
HYB 162-02-02 Complement component C4 (human) 200µl Mouse ELISA, WB
HYB 162-02-1 Complement component C4 (human) 1ml Mouse ELISA, WB
HYB 162-02B-01 Anti-Complement Component C4 100µl Mouse ELISA
HYB 162-04-02 Complement component C4 (human) 200µl Mouse ELISA, WB
HYB 162-04-1 Complement component C4 (human) 1ml Mouse ELISA, WB
HYB 268-01-02 Complement factor H (human, ß1H-globulin) 200µl Mouse ELISA, WB
HYB 268-01-1 Complement factor H (human, ß1H-globulin) 1ml Mouse ELISA, WB
HYB 268-01B-01 Complement factor H (human, ß1H-globulin) 100µl Mouse ELISA
HYB 288-05-02 Complement component C1-inhibitor (C1-INH) 200µl Mouse ELISA
HYB 288-05-1 Complement component C1-inhibitor (C1-INH) 1ml Mouse ELISA
ABS 005-16-02 L-Ficolin (human) 200µl Mouse ELISA, WB
ABS 005-16-1 L-Ficolin (human) 1ml Mouse ELISA, WB
ABS 005-19-02 L-Ficolin (human) 200µl Mouse ELISA, WB, IP
ABS 005-19-1 L-Ficolin (human) 1ml Mouse ELISA, WB, IP
ABS 036-01-02 M-Ficolin (human) 200µl Mouse ELISA, IHC
ABS 036-01-1 M-Ficolin (human) 1ml Mouse ELISA, IHC
ABS 036-05-02 M-Ficolin (human) 200µl Mouse ELISA
ABS 036-05-1 M-Ficolin (human) 1ml Mouse ELISA
RIG 334-01-02 Ficolin H (human) 200µl Mouse ELISA, IP
RIG 334-01-1 Ficolin H (human) 1ml Mouse ELISA, IP
RIG 334-01B-01 Ficolin H (human) 100µl Mouse ELISA
HYB 039-04-02 Properdin (human) 200µl Mouse ELISA, WB
HYB 039-04-1 Properdin (human) 1ml Mouse ELISA, WB
HYB 039-04B-01 Properdin (human) 100µl Mouse ELISA
HYB 213-01-02 Glycoprotein-340 (human, gp-340) 200µl Mouse ELISA, WB, IHC
HYB 213-01-1 Glycoprotein-340 (human, gp-340) 1ml Mouse ELISA, WB, IHC
HYB 213-06-02 Glycoprotein-340 (human, gp-340) 200µl Mouse ELISA, WB, IHC
HYB 213-06-1 Glycoprotein-340 (human, gp-340) 1ml Mouse ELISA, WB, IHC
上海惠诚生物抗原抗体及试剂盒专业客户团队热心为您服务!

 

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